Discussion
Diagnosis With Brief Discussion
- Diagnosis
- UNILATERAL HYPOPLASIA OF THE LUNG
- Radiologic Findings
- Fig 1. Chest roentgenogram shows radio-opacity in the left hemithorax with a mediastinal shift to the same side. Crowding of ribs can be seen on the left side.
Fig 2. Lung window setting of the chest CT scan shows bronchiectatic changes in the small opaque left lung. Compensatory hyperinflation and herniation of the right lung can be seen through the anterior recess.
Fig 3. Mediastinal window setting of the chest contrast CT scan shows the main pulmonary artery and its branches. The left branch of main pulmonary artery is hypoplastic and supplies the herniated right lung.
Fig 4. Mediastinal window setting of the chest contrast CT scan shows right-sided superior and inferior pulmonary veins draining into the left atrium. No demonstrable pulmonary veins can be seen on the left side.
- Brief Review
- Unilateral lung hypoplasia can be primary (idiopathic) or due to secondary causes such as reduced hemithoracic volume, reduced pulmonary perfusion, or reduced fetal respiratory movement (1). Unilateral lung hypoplasia can clinically remain silent until adulthood and is often diagnosed incidentally for non-specific chest complaints (2). Radiological findings in these cases are a marked decrease in the hemithorax with an ipsilateral mediastinal shift and compensatory hyperinflation of the contralateral lung. Aplasia/hypoplasia of pulmonary vessels, bronchi are demonstrated in many cases(1). Typically, the rudimentary lung shows bronchiectatic changes within. Differential diagnoses include severe bronchiectasis with collapse, fibrothorax and atelectasis from other causes. Other differential diagnoses include Swyer James syndrome characterized by a hyperlucent lung with air trapping and Congenital veno-lobar syndrome (Schimitar syndrome) with a hypoplastic lung and the classical 'scimitar' syndrome of an anomalous pulmonary vein draining into the systemic vein (2).
- References
- 1. Kant S. Unilateral pulmonary hypoplasia – a case report. Lung India 2007; 24 : 69-71.
2. Georgescu A, Nuta C, Bondari S. “3D Imaging in Unilateral Primary Pulmonary Hypoplasia in an Adult: A Case Report,” Case Reports in Radiology, vol. 2011, Article ID 659586, 6 pages, 2011. doi:10.1155/2011/659586.
- Keywords
- Lung, Congenital,